enucleation in a patient with neurofibromatosis type 1 with buphthalmos and ocular deformity

Authors

f. asadi-amoli

a. ariapad s. z. tabatabaei

abstract

to report a case of buphthalmos with neurofibromatosis (nf-1) who suffered with blindness suffered enucleation. physical examination & histopathology were performed. physical examination revealed buphthalmos & vascularized cornea with lower lid ectropion and orbital deformity. histopathologic findings shows plexiform neurofibroma in orbital tissue with scleral wall involvement. and hamartomatous proliferation in choroid & cilliary bodies with melanocytic elements. few nf-1 cases with buphthalmos have been reported. but cases with complicationg buphthalmos (retinal detachment & optic nerve atrophy) suffering enucleation are very rare.

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Journal title:
acta medica iranica

جلد ۴۵، شماره ۶، صفحات ۵۱۵-۵۲۰

Keywords
[ ' n e u r o f i b r o m a t o s i s ' , 1 , ' p l e x i f o r m n e u r o f i b r o m a ' , ' b u p h t h a l m o s ' , ' e n u c l e a t i o n ' ]

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